Source | us.nlm.vsac#0.11.0:null (v4.0.1) |
resourceType | ValueSet |
id | 2.16.840.1.113883.3.464.1003.120.11.1003 |
canonical | http://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003 |
version | 20230207 |
status | active |
publisher | NCQA PHEMUR |
name | DisordersOfTheImmuneSystem |
title | Disorders of the Immune System |
date | 2023-02-07T01:03:17-05:00 |
Usages |
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This value set contains 53 concepts
Code | System | Display |
D80.0 | http://hl7.org/fhir/sid/icd-10-cm | Hereditary hypogammaglobulinemia |
D80.1 | http://hl7.org/fhir/sid/icd-10-cm | Nonfamilial hypogammaglobulinemia |
D80.2 | http://hl7.org/fhir/sid/icd-10-cm | Selective deficiency of immunoglobulin A [IgA] |
D80.3 | http://hl7.org/fhir/sid/icd-10-cm | Selective deficiency of immunoglobulin G [IgG] subclasses |
D80.4 | http://hl7.org/fhir/sid/icd-10-cm | Selective deficiency of immunoglobulin M [IgM] |
D80.5 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency with increased immunoglobulin M [IgM] |
D80.6 | http://hl7.org/fhir/sid/icd-10-cm | Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia |
D80.7 | http://hl7.org/fhir/sid/icd-10-cm | Transient hypogammaglobulinemia of infancy |
D80.8 | http://hl7.org/fhir/sid/icd-10-cm | Other immunodeficiencies with predominantly antibody defects |
D80.9 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency with predominantly antibody defects, unspecified |
D81.0 | http://hl7.org/fhir/sid/icd-10-cm | Severe combined immunodeficiency [SCID] with reticular dysgenesis |
D81.1 | http://hl7.org/fhir/sid/icd-10-cm | Severe combined immunodeficiency [SCID] with low T- and B-cell numbers |
D81.2 | http://hl7.org/fhir/sid/icd-10-cm | Severe combined immunodeficiency [SCID] with low or normal B-cell numbers |
D81.4 | http://hl7.org/fhir/sid/icd-10-cm | Nezelof's syndrome |
D81.6 | http://hl7.org/fhir/sid/icd-10-cm | Major histocompatibility complex class I deficiency |
D81.7 | http://hl7.org/fhir/sid/icd-10-cm | Major histocompatibility complex class II deficiency |
D81.82 | http://hl7.org/fhir/sid/icd-10-cm | Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] |
D81.89 | http://hl7.org/fhir/sid/icd-10-cm | Other combined immunodeficiencies |
D81.9 | http://hl7.org/fhir/sid/icd-10-cm | Combined immunodeficiency, unspecified |
D82.0 | http://hl7.org/fhir/sid/icd-10-cm | Wiskott-Aldrich syndrome |
D82.1 | http://hl7.org/fhir/sid/icd-10-cm | Di George's syndrome |
D82.2 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency with short-limbed stature |
D82.3 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency following hereditary defective response to Epstein-Barr virus |
D82.4 | http://hl7.org/fhir/sid/icd-10-cm | Hyperimmunoglobulin E [IgE] syndrome |
D82.8 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency associated with other specified major defects |
D82.9 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency associated with major defect, unspecified |
D83.0 | http://hl7.org/fhir/sid/icd-10-cm | Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function |
D83.1 | http://hl7.org/fhir/sid/icd-10-cm | Common variable immunodeficiency with predominant immunoregulatory T-cell disorders |
D83.2 | http://hl7.org/fhir/sid/icd-10-cm | Common variable immunodeficiency with autoantibodies to B- or T-cells |
D83.8 | http://hl7.org/fhir/sid/icd-10-cm | Other common variable immunodeficiencies |
D83.9 | http://hl7.org/fhir/sid/icd-10-cm | Common variable immunodeficiency, unspecified |
D84.0 | http://hl7.org/fhir/sid/icd-10-cm | Lymphocyte function antigen-1 [LFA-1] defect |
D84.1 | http://hl7.org/fhir/sid/icd-10-cm | Defects in the complement system |
D84.8 | http://hl7.org/fhir/sid/icd-10-cm | Other specified immunodeficiencies |
D84.81 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency due to conditions classified elsewhere |
D84.821 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency due to drugs |
D84.822 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency due to external causes |
D84.89 | http://hl7.org/fhir/sid/icd-10-cm | Other immunodeficiencies |
D84.9 | http://hl7.org/fhir/sid/icd-10-cm | Immunodeficiency, unspecified |
D89.3 | http://hl7.org/fhir/sid/icd-10-cm | Immune reconstitution syndrome |
D89.810 | http://hl7.org/fhir/sid/icd-10-cm | Acute graft-versus-host disease |
D89.811 | http://hl7.org/fhir/sid/icd-10-cm | Chronic graft-versus-host disease |
D89.812 | http://hl7.org/fhir/sid/icd-10-cm | Acute on chronic graft-versus-host disease |
D89.813 | http://hl7.org/fhir/sid/icd-10-cm | Graft-versus-host disease, unspecified |
D89.82 | http://hl7.org/fhir/sid/icd-10-cm | Autoimmune lymphoproliferative syndrome [ALPS] |
D89.831 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade 1 |
D89.832 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade 2 |
D89.833 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade 3 |
D89.834 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade 4 |
D89.835 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade 5 |
D89.839 | http://hl7.org/fhir/sid/icd-10-cm | Cytokine release syndrome, grade unspecified |
D89.89 | http://hl7.org/fhir/sid/icd-10-cm | Other specified disorders involving the immune mechanism, not elsewhere classified |
D89.9 | http://hl7.org/fhir/sid/icd-10-cm | Disorder involving the immune mechanism, unspecified |
Produced 08 Sep 2023