ValueSet-2.16.840.1.113883.3.464.1003.120.11.1003

Sourceus.nlm.vsac#0.11.0:null (v4.0.1)
resourceTypeValueSet
id2.16.840.1.113883.3.464.1003.120.11.1003
canonicalhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.3.464.1003.120.11.1003
version20230207
statusactive
publisherNCQA PHEMUR
nameDisordersOfTheImmuneSystem
titleDisorders of the Immune System
date2023-02-07T01:03:17-05:00
Usages

This value set contains 53 concepts

Code System Display
   D80.0 http://hl7.org/fhir/sid/icd-10-cm Hereditary hypogammaglobulinemia
   D80.1 http://hl7.org/fhir/sid/icd-10-cm Nonfamilial hypogammaglobulinemia
   D80.2 http://hl7.org/fhir/sid/icd-10-cm Selective deficiency of immunoglobulin A [IgA]
   D80.3 http://hl7.org/fhir/sid/icd-10-cm Selective deficiency of immunoglobulin G [IgG] subclasses
   D80.4 http://hl7.org/fhir/sid/icd-10-cm Selective deficiency of immunoglobulin M [IgM]
   D80.5 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency with increased immunoglobulin M [IgM]
   D80.6 http://hl7.org/fhir/sid/icd-10-cm Antibody deficiency with near-normal immunoglobulins or with hyperimmunoglobulinemia
   D80.7 http://hl7.org/fhir/sid/icd-10-cm Transient hypogammaglobulinemia of infancy
   D80.8 http://hl7.org/fhir/sid/icd-10-cm Other immunodeficiencies with predominantly antibody defects
   D80.9 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency with predominantly antibody defects, unspecified
   D81.0 http://hl7.org/fhir/sid/icd-10-cm Severe combined immunodeficiency [SCID] with reticular dysgenesis
   D81.1 http://hl7.org/fhir/sid/icd-10-cm Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
   D81.2 http://hl7.org/fhir/sid/icd-10-cm Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
   D81.4 http://hl7.org/fhir/sid/icd-10-cm Nezelof's syndrome
   D81.6 http://hl7.org/fhir/sid/icd-10-cm Major histocompatibility complex class I deficiency
   D81.7 http://hl7.org/fhir/sid/icd-10-cm Major histocompatibility complex class II deficiency
   D81.82 http://hl7.org/fhir/sid/icd-10-cm Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]
   D81.89 http://hl7.org/fhir/sid/icd-10-cm Other combined immunodeficiencies
   D81.9 http://hl7.org/fhir/sid/icd-10-cm Combined immunodeficiency, unspecified
   D82.0 http://hl7.org/fhir/sid/icd-10-cm Wiskott-Aldrich syndrome
   D82.1 http://hl7.org/fhir/sid/icd-10-cm Di George's syndrome
   D82.2 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency with short-limbed stature
   D82.3 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency following hereditary defective response to Epstein-Barr virus
   D82.4 http://hl7.org/fhir/sid/icd-10-cm Hyperimmunoglobulin E [IgE] syndrome
   D82.8 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency associated with other specified major defects
   D82.9 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency associated with major defect, unspecified
   D83.0 http://hl7.org/fhir/sid/icd-10-cm Common variable immunodeficiency with predominant abnormalities of B-cell numbers and function
   D83.1 http://hl7.org/fhir/sid/icd-10-cm Common variable immunodeficiency with predominant immunoregulatory T-cell disorders
   D83.2 http://hl7.org/fhir/sid/icd-10-cm Common variable immunodeficiency with autoantibodies to B- or T-cells
   D83.8 http://hl7.org/fhir/sid/icd-10-cm Other common variable immunodeficiencies
   D83.9 http://hl7.org/fhir/sid/icd-10-cm Common variable immunodeficiency, unspecified
   D84.0 http://hl7.org/fhir/sid/icd-10-cm Lymphocyte function antigen-1 [LFA-1] defect
   D84.1 http://hl7.org/fhir/sid/icd-10-cm Defects in the complement system
   D84.8 http://hl7.org/fhir/sid/icd-10-cm Other specified immunodeficiencies
   D84.81 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency due to conditions classified elsewhere
   D84.821 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency due to drugs
   D84.822 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency due to external causes
   D84.89 http://hl7.org/fhir/sid/icd-10-cm Other immunodeficiencies
   D84.9 http://hl7.org/fhir/sid/icd-10-cm Immunodeficiency, unspecified
   D89.3 http://hl7.org/fhir/sid/icd-10-cm Immune reconstitution syndrome
   D89.810 http://hl7.org/fhir/sid/icd-10-cm Acute graft-versus-host disease
   D89.811 http://hl7.org/fhir/sid/icd-10-cm Chronic graft-versus-host disease
   D89.812 http://hl7.org/fhir/sid/icd-10-cm Acute on chronic graft-versus-host disease
   D89.813 http://hl7.org/fhir/sid/icd-10-cm Graft-versus-host disease, unspecified
   D89.82 http://hl7.org/fhir/sid/icd-10-cm Autoimmune lymphoproliferative syndrome [ALPS]
   D89.831 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade 1
   D89.832 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade 2
   D89.833 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade 3
   D89.834 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade 4
   D89.835 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade 5
   D89.839 http://hl7.org/fhir/sid/icd-10-cm Cytokine release syndrome, grade unspecified
   D89.89 http://hl7.org/fhir/sid/icd-10-cm Other specified disorders involving the immune mechanism, not elsewhere classified
   D89.9 http://hl7.org/fhir/sid/icd-10-cm Disorder involving the immune mechanism, unspecified

Produced 08 Sep 2023