ValueSet-2.16.840.1.113883.17.4077.2.1008

Sourceus.nlm.vsac#0.11.0:null (v4.0.1)
resourceTypeValueSet
id2.16.840.1.113883.17.4077.2.1008
canonicalhttp://cts.nlm.nih.gov/fhir/ValueSet/2.16.840.1.113883.17.4077.2.1008
version20200820
statusactive
publisherACEP/AMA-PCPI Steward
nameCoagulopathiesExcludingThrombocytopenia
titleCoagulopathies Excluding Thrombocytopenia
date2020-08-20T01:00:47-04:00
experimentalfalse
Usages

This value set contains 199 concepts

Code System Display
   10153004 http://snomed.info/sct Systemic fibrinogenolysis (disorder)
   105604006 http://snomed.info/sct Deficiency of naturally occurring coagulation factor inhibitor (disorder)
   10934005 http://snomed.info/sct Cryofibrinogenemia (disorder)
   111452009 http://snomed.info/sct Postpartum afibrinogenemia with hemorrhage (disorder)
   111589005 http://snomed.info/sct Dysfibrinogenemia (disorder)
   12153008 http://snomed.info/sct Acquired factor IX deficiency disease (disorder)
   123786007 http://snomed.info/sct Blood coagulation disorder with shortened coagulation time (disorder)
   123787003 http://snomed.info/sct Blood coagulation disorder with prolonged coagulation time (disorder)
   123788008 http://snomed.info/sct Blood coagulation disorder with shortened bleeding time (disorder)
   123789000 http://snomed.info/sct Blood coagulation disorder with prolonged bleeding time (disorder)
   123790009 http://snomed.info/sct Blood coagulation disorder with impaired clot retraction time (disorder)
   12546009 http://snomed.info/sct Hemorrhagic disease of the newborn due to vitamin K deficiency (disorder)
   127034005 http://snomed.info/sct Pancytopenia (disorder)
   128088003 http://snomed.info/sct Blood coagulation disorder, categorized by value of screening test (disorder)
   128094006 http://snomed.info/sct Alloimmune platelet transfusion refractoriness (disorder)
   128105004 http://snomed.info/sct von Willebrand disorder (disorder)
   128106003 http://snomed.info/sct Hereditary von Willebrand disease type 1 (disorder)
   128107007 http://snomed.info/sct Hereditary von Willebrand disease type 2 (disorder)
   128108002 http://snomed.info/sct Hereditary von Willebrand disease type 3 (disorder)
   128113003 http://snomed.info/sct Hereditary von Willebrand disease type 1B (disorder)
   128114009 http://snomed.info/sct Hereditary von Willebrand disease type 1C (disorder)
   128115005 http://snomed.info/sct Pseudo von Willebrand disease (disorder)
   1286003 http://snomed.info/sct Vitamin K deficiency coagulation disorder (disorder)
   13507004 http://snomed.info/sct Purpura fulminans (disorder)
   13993001 http://snomed.info/sct Factor XIII inhibitor disorder (disorder)
   14230004 http://snomed.info/sct Acquired factor VIII deficiency disease (disorder)
   15132005 http://snomed.info/sct Acquired factor XII deficiency disease (disorder)
   154818001 http://snomed.info/sct Congenital afibrinogenemia (disorder)
   1563006 http://snomed.info/sct Protein S deficiency disease (disorder)
   16773005 http://snomed.info/sct Drug-induced coagulation inhibitor disorder (disorder)
   16872008 http://snomed.info/sct Severe hereditary factor VIII deficiency disease (disorder)
   16922007 http://snomed.info/sct Hereditary coagulation factor deficiency (disorder)
   180481005 http://snomed.info/sct Anti-factor II disorder (disorder)
   181456001 http://snomed.info/sct Antiprothrombin disorder (disorder)
   183005 http://snomed.info/sct Autoimmune pancytopenia (disorder)
   18604004 http://snomed.info/sct Factor XIII deficiency disease (disorder)
   191296000 http://snomed.info/sct Deficiency of coagulation factor due to liver disease (disorder)
   191297009 http://snomed.info/sct Deficiency of coagulation factor due to vitamin K deficiency (disorder)
   191298004 http://snomed.info/sct Acquired factor II deficiency (disorder)
   19267009 http://snomed.info/sct Lupus anticoagulant disorder (disorder)
   200030007 http://snomed.info/sct Postpartum coagulation defects - delivered with postnatal problem (disorder)
   200031006 http://snomed.info/sct Postpartum coagulation defects with postnatal problem (disorder)
   2036003 http://snomed.info/sct Acquired factor VII deficiency disease (disorder)
   21360006 http://snomed.info/sct Miscarriage with afibrinogenemia (disorder)
   234367000 http://snomed.info/sct Pancytopenia with pancreatitis (disorder)
   234440005 http://snomed.info/sct Factor VIII deficiency (disorder)
   234442002 http://snomed.info/sct Hereditary factor VIII deficiency disease with inhibitor (disorder)
   234444001 http://snomed.info/sct Congenital factor IX deficiency variant (disorder)
   234445000 http://snomed.info/sct Congenital factor IX deficiency with inhibitor (disorder)
   234451005 http://snomed.info/sct Acquired von Willebrand disease (disorder)
   234452003 http://snomed.info/sct Contact factor deficiency (disorder)
   234453008 http://snomed.info/sct Passovoy factor deficiency (disorder)
   234454002 http://snomed.info/sct Prothrombin complex deficiency (disorder)
   234455001 http://snomed.info/sct Fibrinogen abnormality (disorder)
   234456000 http://snomed.info/sct Congenital fibrinogen abnormality (disorder)
   234457009 http://snomed.info/sct Hypofibrinogenemia (disorder)
   234458004 http://snomed.info/sct Hypodysfibrinogenemia (disorder)
   234459007 http://snomed.info/sct Alpha chain defect dysfibrinogenemia (disorder)
   234460002 http://snomed.info/sct Beta chain defect dysfibrinogenemia (disorder)
   234461003 http://snomed.info/sct Gamma chain defect dysfibrinogenemia (disorder)
   234462005 http://snomed.info/sct Acquired fibrinogen abnormality (disorder)
   234463000 http://snomed.info/sct Combined coagulation factor deficiency (disorder)
   234464006 http://snomed.info/sct Fibrinolytic bleeding syndrome (disorder)
   234465007 http://snomed.info/sct Alpha-2-antiplasmin deficiency (disorder)
   234466008 http://snomed.info/sct Acquired coagulation disorder (disorder)
   234486007 http://snomed.info/sct Montreal platelet syndrome (disorder)
   237336007 http://snomed.info/sct Fibrinolysis - postpartum (disorder)
   237337003 http://snomed.info/sct Afibrinogenemia - postpartum (disorder)
   24149006 http://snomed.info/sct Hemorrhagic disease of the newborn due to factor II deficiency (disorder)
   25904003 http://snomed.info/sct Acquired coagulation factor deficiency (disorder)
   26029002 http://snomed.info/sct Mild hereditary factor VIII deficiency disease (disorder)
   267272006 http://snomed.info/sct Postpartum coagulation defects (disorder)
   27068000 http://snomed.info/sct Failed attempted abortion with afibrinogenemia (disorder)
   27312002 http://snomed.info/sct High molecular weight kininogen deficiency (disorder)
   278504009 http://snomed.info/sct Afibrinogenemia (disorder)
   282707003 http://snomed.info/sct Acquired inhibitor of coagulation (disorder)
   28293008 http://snomed.info/sct Hereditary factor VIII deficiency disease (disorder)
   296926001 http://snomed.info/sct Heparin overdose (disorder)
   30575002 http://snomed.info/sct Fanconi's anemia (disorder)
   307514008 http://snomed.info/sct Idiopathic factor VIII deficiency (disorder)
   307515009 http://snomed.info/sct Autoimmune factor VIII deficiency (disorder)
   307517001 http://snomed.info/sct Pregnancy-related factor VIII deficiency (disorder)
   307518006 http://snomed.info/sct Malignancy-related factor VIII deficiency (disorder)
   31925001 http://snomed.info/sct Hereditary factor I deficiency disease (disorder)
   32605001 http://snomed.info/sct Transient neonatal disorder of coagulation (disorder)
   33169001 http://snomed.info/sct Factor XI deficiency, type II (disorder)
   33297000 http://snomed.info/sct Hereditary factor II deficiency disease (disorder)
   33344008 http://snomed.info/sct Moderate hereditary factor VIII deficiency disease (disorder)
   33820001 http://snomed.info/sct Acquired factor X deficiency disease (disorder)
   34417008 http://snomed.info/sct Disseminated intravascular coagulation in newborn (disorder)
   34478009 http://snomed.info/sct Failed attempted abortion with defibrination syndrome (disorder)
   35554008 http://snomed.info/sct Acquired factor XI deficiency disease (disorder)
   359536009 http://snomed.info/sct Megakaryocytic aplasia (disorder)
   359700009 http://snomed.info/sct Hereditary von Willebrand disease type 1A (disorder)
   359711001 http://snomed.info/sct Hereditary von Willebrand disease type 2A (disorder)
   359717002 http://snomed.info/sct Hereditary von Willebrand disease type 2B (disorder)
   359723007 http://snomed.info/sct Acquired hypofibrinogenemia (disorder)
   359725000 http://snomed.info/sct Hereditary von Willebrand disease type 2M (disorder)
   359727008 http://snomed.info/sct Fibrinogen deficiency (disorder)
   359730001 http://snomed.info/sct Acquired afibrinogenemia (disorder)
   359732009 http://snomed.info/sct Hereditary von Willebrand disease type 2N (disorder)
   36351005 http://snomed.info/sct Antithrombin III deficiency (disorder)
   37193007 http://snomed.info/sct Factor VII deficiency (disorder)
   373420004 http://snomed.info/sct Upshaw-Schulman syndrome (disorder)
   37350004 http://snomed.info/sct Hereditary factor X deficiency disease (disorder)
   3760002 http://snomed.info/sct Familial multiple factor deficiency syndrome, type V (disorder)
   38879000 http://snomed.info/sct Factor XI inhibitor disorder (disorder)
   38970002 http://snomed.info/sct Doan-Wright syndrome (disorder)
   402851000 http://snomed.info/sct Neonatal purpura fulminans due to homozygous protein C deficiency (disorder)
   40855001 http://snomed.info/sct Hereditary factor VII deficiency disease (disorder)
   41106001 http://snomed.info/sct von Willebrand factor inhibitor disorder (disorder)
   41690001 http://snomed.info/sct Factor V inhibitor disorder (disorder)
   41788008 http://snomed.info/sct Hereditary factor IX deficiency disease (disorder)
   41816006 http://snomed.info/sct Secondary cryofibrinogenemia (disorder)
   425949001 http://snomed.info/sct Mild hereditary factor VIII deficiency disease with inhibitor (disorder)
   426199009 http://snomed.info/sct Congenital factor IX deficiency without inhibitor (disorder)
   4320005 http://snomed.info/sct Factor V deficiency (disorder)
   43217004 http://snomed.info/sct Hereditary factor XII deficiency disease (disorder)
   438360006 http://snomed.info/sct Hereditary factor VIII deficiency disease without inhibitor (disorder)
   438372000 http://snomed.info/sct Hereditary factor IX deficiency disease with inhibitor (disorder)
   438373005 http://snomed.info/sct Severe hereditary factor VIII deficiency disease with inhibitor (disorder)
   438599002 http://snomed.info/sct Moderate hereditary factor VIII deficiency disease with inhibitor (disorder)
   438792009 http://snomed.info/sct Hereditary factor IX deficiency disease without inhibitor (disorder)
   438827002 http://snomed.info/sct Hereditary thrombophilic dysfibrinogenemia (disorder)
   439000005 http://snomed.info/sct Hyperfibrinogenemia (disorder)
   439145006 http://snomed.info/sct Congenital hypofibrinogenemia (disorder)
   439156006 http://snomed.info/sct Acquired combined coagulation factor deficiency (disorder)
   439157002 http://snomed.info/sct Hereditary combined coagulation factor deficiency (disorder)
   439274008 http://snomed.info/sct Hereditary protein C deficiency (disorder)
   439455002 http://snomed.info/sct Hereditary factor XIII A subunit deficiency (disorder)
   439458000 http://snomed.info/sct Factor I deficiency disease (disorder)
   439459008 http://snomed.info/sct Hereditary factor XIII B subunit deficiency (disorder)
   439460003 http://snomed.info/sct Hereditary factor XIII A subunit and B subunit deficiency (disorder)
   439699000 http://snomed.info/sct Hereditary antithrombin III deficiency (disorder)
   439702007 http://snomed.info/sct Hereditary protein S deficiency (disorder)
   440820004 http://snomed.info/sct Mild hereditary factor VIII deficiency disease without inhibitor (disorder)
   440866009 http://snomed.info/sct Severe hereditary factor IX deficiency disease with inhibitor (disorder)
   440867000 http://snomed.info/sct Moderate hereditary factor IX deficiency disease with inhibitor (disorder)
   440868005 http://snomed.info/sct Mild hereditary factor IX deficiency disease with inhibitor (disorder)
   440924009 http://snomed.info/sct Hereditary hyperfibrinogenemia (disorder)
   440988005 http://snomed.info/sct Heterozygous protein S deficiency (disorder)
   440993008 http://snomed.info/sct Severe hereditary factor VIII deficiency disease without inhibitor (disorder)
   441006000 http://snomed.info/sct Moderate hereditary factor VIII deficiency disease without inhibitor (disorder)
   441101007 http://snomed.info/sct Heterozygous protein C deficiency (disorder)
   441188004 http://snomed.info/sct Homozygous protein C deficiency (disorder)
   441189007 http://snomed.info/sct Homozygous protein S deficiency (disorder)
   441190003 http://snomed.info/sct Severe hereditary factor IX deficiency disease without inhibitor (disorder)
   441191004 http://snomed.info/sct Moderate hereditary factor IX deficiency disease without inhibitor (disorder)
   441192006 http://snomed.info/sct Mild hereditary factor IX deficiency disease without inhibitor (disorder)
   45366001 http://snomed.info/sct Hereditary dysfibrinogenemia (disorder)
   45963004 http://snomed.info/sct Factor XI deficiency, type III (disorder)
   46760003 http://snomed.info/sct Estren-Dameshek anemia (disorder)
   46981006 http://snomed.info/sct Factor XII deficiency disease (disorder)
   47307007 http://snomed.info/sct Factor VIII inhibitor disorder (disorder)
   48976006 http://snomed.info/sct Prekallikrein deficiency (disorder)
   49177006 http://snomed.info/sct Postpartum coagulation defect with hemorrhage (disorder)
   49762007 http://snomed.info/sct Hereditary factor XI deficiency disease (disorder)
   50189006 http://snomed.info/sct Hereditary factor XIII deficiency disease (disorder)
   50770000 http://snomed.info/sct Miscarriage with defibrination syndrome (disorder)
   58327003 http://snomed.info/sct Factor I inhibitor disorder (disorder)
   5876000 http://snomed.info/sct Acquired pancytopenia (disorder)
   61551003 http://snomed.info/sct Familial multiple factor deficiency syndrome, type VI (disorder)
   61802005 http://snomed.info/sct Primary cryofibrinogenemia (disorder)
   62698000 http://snomed.info/sct Defibrination syndrome following molar AND/OR ectopic pregnancy (disorder)
   6364000 http://snomed.info/sct Acquired factor XIII deficiency disease (disorder)
   64315007 http://snomed.info/sct Familial multiple factor deficiency syndrome, type III (disorder)
   64509006 http://snomed.info/sct Acquired coagulation factor inhibitor disorder (disorder)
   64779008 http://snomed.info/sct Blood coagulation disorder (disorder)
   65768009 http://snomed.info/sct Familial multiple factor deficiency syndrome, type II (disorder)
   66909001 http://snomed.info/sct Familial multiple factor deficiency syndrome, type IV (disorder)
   67406007 http://snomed.info/sct Disseminated intravascular coagulation (disorder)
   6935003 http://snomed.info/sct Familial hemorrhagic diathesis (disorder)
   69500007 http://snomed.info/sct Blood coagulation disorder due to liver disease (disorder)
   73162004 http://snomed.info/sct Posttransfusion purpura (disorder)
   73975000 http://snomed.info/sct Factor II deficiency (disorder)
   75331009 http://snomed.info/sct Evans syndrome (disorder)
   76407009 http://snomed.info/sct Protein C deficiency disease (disorder)
   76642003 http://snomed.info/sct Factor X deficiency (disorder)
   79674009 http://snomed.info/sct Hyperheparinemia (disorder)
   80988005 http://snomed.info/sct Mixed cryofibrinogenemia (disorder)
   81783000 http://snomed.info/sct Familial multiple factor deficiency syndrome (disorder)
   84048006 http://snomed.info/sct Familial multiple factor deficiency syndrome, type I (disorder)
   85796009 http://snomed.info/sct Afibrinogenemia following molar AND/OR ectopic pregnancy (disorder)
   86075001 http://snomed.info/sct Coagulation factor deficiency syndrome (disorder)
   86635005 http://snomed.info/sct Kasabach-Merritt syndrome (disorder)
   88540000 http://snomed.info/sct Factor XI deficiency, type I (disorder)
   88776002 http://snomed.info/sct Hereditary factor V deficiency disease (disorder)
   89729000 http://snomed.info/sct Factor IX inhibitor disorder (disorder)
   90935002 http://snomed.info/sct Hemophilia (disorder)
   9489006 http://snomed.info/sct Factor X inhibitor disorder (disorder)
   95605009 http://snomed.info/sct Hemolysis-elevated liver enzymes-low platelet count syndrome (disorder)
   95623001 http://snomed.info/sct Neonatal coagulation disorder (disorder)
   95839005 http://snomed.info/sct Disorder involving the fibrinolytic system (disorder)
   95840007 http://snomed.info/sct Hypoplasminogenemia (disorder)
   95841006 http://snomed.info/sct Hereditary hypoplasminogenemia (disorder)
   95842004 http://snomed.info/sct Autosomal dominant deficiency of plasminogen (disorder)
   95843009 http://snomed.info/sct Acquired hypoplasminogenemia (disorder)
   95844003 http://snomed.info/sct Dysplasminogenemia (disorder)
   95845002 http://snomed.info/sct Hereditary dysplasminogenemia (disorder)

Produced 08 Sep 2023